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Author Kræmer, Pia ♦ Grønbæk, Henning ♦ Kievit, Linda ♦ Hamiltondutoit, Stephen
Source Directory of Open Access Journals (DOAJ)
Content type Text
Publisher Karger Publishers
File Format HTM / HTML
Date Created 2018-02-02
Copyright Year ©2018
Language English
Subject Domain (in LCC) RC799-869
Subject Keyword Portal hypertension ♦ Ascites ♦ Noncirrhotic portal hypertension ♦ Wilms’ tumor ♦ Internal medicine ♦ Diseases of the digestive system ♦ Medicine ♦ Gastroenterology ♦ Specialties of internal medicine
Abstract A 37-year-old male, who at the age of 8 years had been treated for right-sided Wilms’ tumor with nephrectomy, radiotherapy, and chemotherapy, presented with noncirrhotic portal hypertension (NCPH), grade 2 esophageal varices, and ascites. A CT scan demonstrated hypoplasia of liver segments 2 and 3. A liver biopsy showed portal tract fibrosis without cirrhosis, with histological features of NCPH. Liver vein catheterization showed a normal portal pressure gradient of 5 mm Hg while spleen to hepatic vein pressure was 29 mm Hg. NCPH after therapy for Wilms’ tumor is described in children within the first few years after treatment. This is the first case report in which the patient first presented symptoms as an adult, many years after cancer treatment.
ISSN 16620631
Age Range 18 to 22 years ♦ above 22 year
Educational Use Research
Education Level UG and PG ♦ Career/Technical Study
Learning Resource Type Article
Publisher Date 2018-02-01
e-ISSN 16620631
Journal Case Reports in Gastroenterology
Volume Number 12
Issue Number 1
Page Count 7
Starting Page 56
Ending Page 62

Source: Directory of Open Access Journals (DOAJ)